Heart transplantation in single-ventricle physiology with failed fontan circulation
نویسندگان
چکیده
Methods Between 1986 and 2011, 179 children underwent heart transplantation for cardiomyopathy and end-stage congenital heart disease. Fifteen patients had single-ventricle physiology and underwent Fontan procedure. Five patients (mean age 6.6±1.2, range 2-14, years old) had failed Fontan circulation. Interval between Fontan procedure and failing circulation was 8-14 years. Indications for heart transplantation were ventricular failure (n=4), and protein-losing enteropathy (n=1).
منابع مشابه
Orthotopic Heart Transplantation in Patients with Univentricular Physiology
Parallel advancements in surgical technique, preoperative and postoperative care, as well as a better understanding of physiology in patients with duct-dependent pulmonary or systemic circulation and a functional single ventricle, have led to superb results in staged palliation of most complex congenital heart disease (CHD) [1]. The Fontan procedure and its technical modifications have resulted...
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